William-Beuren Syndrome (WBS) is a rare genetic syndrome with a multisystemic disorder, including abnormalities, intellectual disability, and cardiovascular disease. The prevalence is around 1 in 10,000 live births, but it could be higher since it is undiagnosed. Dental manifestations in this syndrome are malocclusion, enamel hypoplasia, malformed teeth, and dental caries.
Dental caries was the most common oral disorder leading to a person™s lower life quality, both aesthetically and functionally. Pediatric dentists are in charge of treating children with special needs, especially with complex cases. The dental treatment in children with heart defects must be carried out with caution, considering that these conditions can increase the risk of infective endocarditis. Dental care must be carried out comprehensively by involving a cardiologist to help determine treatment procedures, such as prophylactic antibiotics.
Comprehensive dental treatment under general anesthesia is recommended for children with cardiac abnormalities, especially in cases of multiple caries. General anesthesia refers to the loss of protective reflexes that render a person unconscious after administration of anesthetic drugs by maintaining the airway and responding to stimuli. Giving general anesthesia to treat children with special needs can improve the quality of dental care, especially preventing children from stress.
Author: Tania Saskianti, drg., Ph.D., Sp.KGA, K-AIBK
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